Dandy-Walker Syndrome

Synonyms

Cyst, Dandy-Walker

Cysts, Dandy-Walker

Dandy Walker Complex

Dandy Walker Deformity

Dandy Walker Malformation

Dandy Walker Syndrome

Dandy Walker Syndrome, Familial

Dandy-Walker Complex

Dandy-Walker Complices

Dandy-Walker Cyst

Dandy-Walker Cysts

Dandy-Walker Deformities

Dandy-Walker Deformity

Dandy-Walker Malformation

Dandy-Walker Syndrome, Familial

Familial Dandy-Walker Syndrome

Hydrocephalus, Internal, Dandy-Walker Type

Hydrocephalus, Noncommunicating, Dandy-Walker Type

Luschka Magendie Foramina Atresia

Luschka-Magendie Foramina Atresia

Malformation, Dandy-Walker

A congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. Clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (From Menkes, Textbook of Child Neurology, 5th ed, pp294-5)