Erythrokeratodermia Variabilis

Synonyms

Erythro et Keratodermia Variabilis

Erythrokeratodermia Figurata Variabilis

Erythrokeratodermia Figurata, Congenital Familial, in Plaqus

Erythrokeratodermia Variabilis with Erythema Gyratum Repens

Erythrokeratodermia, Progressive Symmetric

Greither Disease

Mendes De Costa Syndrome

Progressive Symmetric Erythrokeratodermia

Transgrediens et Progrediens Palmoplantar Keratoderma

An autosomal dominant skin disease characterized by transient and variable noninflammatory ERYTHEMA and hyperkeratosis. It has been associated with mutations in the genes that code for CONNEXINS. Erythrokeratodermia variabilis inherited in an autosomal recessive fashion has also been reported. Affected individuals often develop PALMOPLANTAR KERATODERMA.