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Hunter Syndrome Gargoylism

Systemic Lysosomal Storage Disease marked by progressive physical deterioration and caused by a deficiency of L-Sulfoiduronate Sulfatase. This Disease differs from Mucopolysaccharidosis I by slower progression, lack of corneal clouding, and X-linked rather than autosomal recessive inheritance. The mild form produces near-normal Intelligence and Life span. The severe form usually causes Death by age 15.