Idiopathic Pulmonary Fibrosis
Synonyms
Cryptogenic Fibrosing Alveolitides
Cryptogenic Fibrosing Alveolitis
Disease, Hamman-Rich
Diseases, Hamman-Rich
Dysplasia, Fibrocystic Pulmonary
Dysplasias, Fibrocystic Pulmonary
Familial Idiopathic Pulmonary Fibrosis
Fibrocystic Pulmonary Dysplasia
Fibrocystic Pulmonary Dysplasias
Fibrosing Alveolitides, Cryptogenic
Fibrosing Alveolitis, Cryptogenic
Hamman Rich Disease
Hamman-Rich Disease
Hamman-Rich Diseases
Idiopathic Fibrosing Alveolitis, Chronic Form
Idiopathic Pulmonary Fibroses
Idiopathic Pulmonary Fibrosis, Familial
Interstitial Pneumonia, Usual
Interstitial Pneumonias, Usual
Interstitial Pneumonitides, Usual
Interstitial Pneumonitis, Usual
Pneumonitides, Usual Interstitial
Pneumonitis, Usual Interstitial
Pulmonary Dysplasia, Fibrocystic
Pulmonary Dysplasias, Fibrocystic
Pulmonary Fibroses, Idiopathic
Pulmonary Fibrosis, Idiopathic
Usual Interstitial Pneumonia
Usual Interstitial Pneumonias
Usual Interstitial Pneumonitides
Usual Interstitial Pneumonitis
A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.