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MMSA Dehydrogenase

An enzyme that plays a Role in the Valine; Leucine; and Isoleucine catabolic pathways by catalyzing the oxidation of 2-methyl-3-oxopropanate to propanoyl-CoA using NAD+ as a coenzyme. Methylmalonate semialdehyde Dehydrogenase deficiency is characterized by elevated beta-Alanine and 3-hydropropionic acid.