Wiskott-Aldrich Syndrome

Synonyms

Aldrich Syndrome

Eczema Thrombocytopenia Immunodeficiency Syndrome

Eczema-Thrombocytopenia-Immunodeficiency Syndrome

Eczema-Thrombocytopenia-Immunodeficiency Syndromes

Imd2

Immunodeficiency 2

Syndrome, Aldrich

Syndrome, Eczema-Thrombocytopenia-Immunodeficiency

Syndrome, Wiskott-Aldrich

Syndromes, Eczema-Thrombocytopenia-Immunodeficiency

Wiskott Aldrich Syndrome

Wiskott Syndrome

A rare, X-linked immunodeficiency syndrome characterized by ECZEMA; LYMPHOPENIA; and, recurrent pyogenic infection. It is seen exclusively in young boys. Typically, IMMUNOGLOBULIN M levels are low and IMMUNOGLOBULIN A and IMMUNOGLOBULIN E levels are elevated. Lymphoreticular malignancies are common.