Complement C1 Inhibitor Protein
C1 Esterase Inhibitor
C1 INH Protein
C1 Inhibitor Protein
Complement C1-Inhibitor Protein
Esterase Inhibitor, C1
Plasma Protease C1 Inhibitor
An endogenous 105-kDa plasma glycoprotein produced primarily by the LIVER and MONOCYTES. It inhibits a broad spectrum of proteases, including the COMPLEMENT C1R and the COMPLEMENT C1S proteases of the CLASSICAL COMPLEMENT PATHWAY, and the MANNOSE-BINDING PROTEIN-ASSOCIATED SERINE PROTEASES. C1-INH-deficient individuals suffer from HEREDITARY ANGIOEDEMA TYPES I AND II.