Creutzfeldt-Jakob Syndrome
Synonyms
CJD (Creutzfeldt Jakob Disease)
CJD (Creutzfeldt-Jakob Disease)
Creutzfeldt Jacob Disease
Creutzfeldt Jakob Disease
Creutzfeldt Jakob Disease, Familial
Creutzfeldt Jakob Disease, New Variant
Creutzfeldt Jakob Disease, Variant
Creutzfeldt Jakob Syndrome
Creutzfeldt-Jakob Disease
Creutzfeldt-Jakob Disease, Familial
Creutzfeldt-Jakob Disease, New Variant
Creutzfeldt-Jakob Disease, Variant
Creutzfeldt-Jakob Diseases, Familial
Disease, Creutzfeldt Jacob
Disease, Creutzfeldt-Jakob
Disease, Familial Creutzfeldt-Jakob
Disease, Jakob-Creutzfeldt
Encephalopathies, Subacute Spongiform
Encephalopathy, Subacute Spongiform
Familial Creutzfeldt Jakob Disease
Familial Creutzfeldt-Jakob Disease
Familial Creutzfeldt-Jakob Diseases
Jacob Disease, Creutzfeldt
Jakob Creutzfeldt Disease
Jakob Creutzfeldt Syndrome
Jakob-Creutzfeldt Disease
Jakob-Creutzfeldt Syndrome
New Variant Creutzfeldt Jakob Disease
New Variant Creutzfeldt-Jakob Disease
Spongiform Encephalopathies, Subacute
Spongiform Encephalopathy, Subacute
Subacute Spongiform Encephalopathies
Subacute Spongiform Encephalopathy
Syndrome, Creutzfeldt-Jakob
Syndrome, Jakob-Creutzfeldt
V CJD (Variant Creutzfeldt Jakob Disease)
V-CJD (Variant-Creutzfeldt-Jakob Disease)
Variant Creutzfeldt Jakob Disease
Variant Creutzfeldt-Jakob Disease
A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))