Denys-Drash Syndrome
Synonyms
Denys Drash Syndrome
Drash Syndrome
Nephropathy, Wilms Tumor, and Genital Anomalies
Pseudohermaphroditism, Nephron Disorder and Wilms' Tumor
Syndrome, Denys-Drash
Syndrome, Drash
Wilms Tumor and Pseudohermaphroditism
A disorder of sex development characterized by UROGENITAL ABNORMALITIES; GONADAL DYSGENESIS; and WILMS TUMOR. It is caused by a mutation in the Wilms tumor suppressor gene (GENES, WILMS TUMOR) on chromosome 11.
See Also