Incontinentia Pigmenti

Synonyms

Bloch Sulzberger Syndrome

Bloch-Siemens Syndrome

Bloch-Siemens-Sulzberger Syndrome

Bloch-Sulzberger Syndrome

Syndrome, Bloch-Sulzberger

A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.