CoA Dehydrogenase, Isovaleryl
Dehydrogenase, Isovaleryl CoA
Dehydrogenase, Isovaleryl-Coenzyme A
Isovaleryl CoA Dehydrogenase
Isovaleryl Coenzyme A Dehydrogenase
Isovaleryl-Coenzyme A Dehydrogenase
A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).