Jaundice, Chronic Idiopathic


Chronic Idiopathic Jaundice

Chronic Idiopathic Jaundices

Dubin Johnson Syndrome

Dubin-Johnson Syndrome

Hyperbilirubinemia 2

Hyperbilirubinemia 2s

Hyperbilirubinemia II

Hyperbilirubinemia IIs

Idiopathic Jaundice, Chronic

Idiopathic Jaundices, Chronic

Jaundices, Chronic Idiopathic

Syndrome, Dubin-Johnson

A benign, autosomally recessive inherited hyperbilirubinemia characterized by the presence of a dark pigment in the centrilobular region of the liver cells. There is a functional defect in biliary excretion of bilirubin, cholephilic dyes, and porphyrins. Affected persons may be asymptomatic or have vague constitutional or gastrointestinal symptoms. The liver may be slightly enlarged, and oral and intravenous cholangiography fails to visualize the biliary tract.