Malignant Atrophic Papulosis


Atrophic Papuloses, Malignant

Atrophic Papulosis, Malignant

Degos Disease

Degos Syndrome

Degos's Malignant Atrophic Papulosis

Disease, Degos

Disease, Kohlmeier-Degos

Erythrokeratoderma en cocardes

Kohlmeier-Degos Disease

Malignant Atrophic Papuloses

Papuloses, Malignant Atrophic

Papulosis, Malignant Atrophic

Syndrome, Degos

Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.