Myoclonic Cerebellar Dyssynergia


Ataxia, Dentate Cerebellar

Ataxias, Dentate Cerebellar

Atrophies, Dentate Cerebellar

Atrophy, Dentate Cerebellar

Cerebellar Ataxias, Dentate

Cerebellar Atrophy, Dentate

Cerebellar Dyssynergia

Cerebellar Dyssynergia, Myoclonic

Cerebellar Dyssynergias

Cerebellar Dyssynergias, Myoclonic

Cerebelloparenchymal Disorder V

Dentate Cerebellar Ataxia

Dentate Cerebellar Ataxias

Dentate Cerebellar Atrophies

Dentate Cerebellar Atrophy

Dentate Nucleus Syndrome, Ramsay Hunt

Dyssynergia Cerebellaris Myoclonica

Dyssynergia Cerebellaris Myoclonica Of Hunt

Dyssynergia Cerebellaris Progressiva

Dyssynergia, Cerebellar

Dyssynergia, Myoclonic Cerebellar

Dyssynergias, Cerebellar

Dyssynergias, Myoclonic Cerebellar

Myoclonic Cerebellar Dyssynergias

Ramsay Hunt Cerebellar Syndrome

Ramsay Hunt Dentate Syndrome

Spinodentate Atrophy

A condition marked by progressive CEREBELLAR ATAXIA combined with MYOCLONUS usually presenting in the third decade of life or later. Additional clinical features may include generalized and focal SEIZURES, spasticity, and DYSKINESIAS. Autosomal recessive and autosomal dominant patterns of inheritance have been reported. Pathologically, the dentate nucleus and brachium conjunctivum of the CEREBELLUM are atrophic, with variable involvement of the spinal cord, cerebellar cortex, and basal ganglia. (From Joynt, Clinical Neurology, 1991, Ch37, pp60-1)