Trihexosylceramides
Synonyms
Ceramide Trihexosides
Ceramides, Trihexosyl
Trihexosides, Ceramide
Trihexosyl Ceramides
Glycosphingolipids which contain as their polar head group a trisaccharide (galactose-galactose-glucose) moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in ceramide trihexosidase, is the cause of angiokeratoma corporis diffusum (FABRY DISEASE).