Uroporphyrinogen III Synthetase



Cosynthetase, Uroporphyrinogen III

Hydroxymethylbilane hydro-lyase (cyclizing)

Isomerase, Uroporphyrinogen

Synthase, Uroporphyrinogen-III

Synthetase, Uroporphyrinogen III

Uroporphyrinogen III Cosynthetase

Uroporphyrinogen III Synthase

Uroporphyrinogen Isomerase

Uroporphyrinogen-III Synthase

An enzyme that catalyzes the cyclization of hydroxymethylbilane to yield UROPORPHYRINOGEN III and water. It is the fourth enzyme in the 8-enzyme biosynthetic pathway of HEME, and is encoded by UROS gene. Mutations of UROS gene result in CONGENITAL ERYTHROPOIETIC PORPHYRIA.