Cystic Fibrosis


Cystic Fibrosis of Pancreas

Cystic Fibrosis, Pancreatic

Cystic Fibrosis, Pulmonary

Fibrocystic Disease of Pancreas

Fibrosis, Cystic


Pancreas Fibrocystic Disease

Pancreas Fibrocystic Diseases

Pancreatic Cystic Fibrosis

Pulmonary Cystic Fibrosis

An autosomal recessive genetic disease of the EXOCRINE GLANDS. It is caused by mutations in the gene encoding the CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR expressed in several organs including the LUNG, the PANCREAS, the BILIARY SYSTEM, and the SWEAT GLANDS. Cystic fibrosis is characterized by epithelial secretory dysfunction associated with ductal obstruction resulting in AIRWAY OBSTRUCTION; chronic RESPIRATORY INFECTIONS; PANCREATIC INSUFFICIENCY; maldigestion; salt depletion; and HEAT PROSTRATION.