Hemophilia B
Synonyms
Bs, Hemophilia
Christmas Disease
Deficiencies, F9
Deficiencies, Factor IX
Deficiency, F9
Deficiency, Factor IX
Disease, Christmas
F9 Deficiencies
F9 Deficiency
Factor IX Deficiencies
Factor IX Deficiency
Haemophilia B
Haemophilia Bs
Hemophilia B Leyden
Hemophilia B(M)
Hemophilia Bs
Hemophilia Bs (M)
Plasma Thromboplastin Component Deficiency
A deficiency of blood coagulation factor IX inherited as an X-linked disorder. (Also known as Christmas Disease, after the first patient studied in detail, not the holy day.) Historical and clinical features resemble those in classic hemophilia (HEMOPHILIA A), but patients present with fewer symptoms. Severity of bleeding is usually similar in members of a single family. Many patients are asymptomatic until the hemostatic system is stressed by surgery or trauma. Treatment is similar to that for hemophilia A. (From Cecil Textbook of Medicine, 19th ed, p1008)
See Also