Sarcosine Dehydrogenase
Synonyms
Dehydrogenase, Monomethylglycine
Dehydrogenase, Sarcosine
Monomethylglycine Dehydrogenase
N-Demethylase, Sarcosine
Sarcosine N Demethylase
Sarcosine N-Demethylase
A LIVER mitochondrial matrix flavoenzyme that catalyzes the oxidation of SARCOSINE to GLYCINE and FORMALDEHYDE. Mutation in the enzyme causes sarcosinemia, a rare autosomal metabolic defect characterized by elevated levels of SARCOSINE in BLOOD and URINE.