Bulbar Palsy, Progressive


Bulbar Palsies

Bulbar Palsies, Progressive

Bulbar Palsy

Bulbar Palsy, Progressive, Of Childhood

Bulbar Paralyses

Bulbar Paralysis

Childhood Progressive Bulbar Palsy

Fazio Londe Disease

Fazio Londe Syndrome

Fazio-Londe Disease

Fazio-Londe Syndrome

Palsies, Bulbar

Palsies, Progressive Bulbar

Palsy, Bulbar

Palsy, Progressive Bulbar

Paralysis, Bulbar

Progressive Bulbar Palsies

Progressive Bulbar Palsy

Progressive Bulbar Palsy of Childhood

A motor neuron disease marked by progressive weakness of the muscles innervated by cranial nerves of the lower brain stem. Clinical manifestations include dysarthria, dysphagia, facial weakness, tongue weakness, and fasciculations of the tongue and facial muscles. The adult form of the disease is marked initially by bulbar weakness which progresses to involve motor neurons throughout the neuroaxis. Eventually this condition may become indistinguishable from AMYOTROPHIC LATERAL SCLEROSIS. Fazio-Londe syndrome is an inherited form of this illness which occurs in children and young adults. (Adams et al., Principles of Neurology, 6th ed, p1091; Brain 1992 Dec;115(Pt 6):1889-1900)